Journal of Anaesthesia & Critical Care Case Reports

Vol 7 | Issue 3 | September-December 2021 | Page: 23-25 | Shilpi Sethi, Manish Sethi

DOI: 10.13107/jaccr.2021.v07i03.188

Author: Shilpi Sethi [1], Manish Sethi [2]

[1] Department of Anaesthesia, Brighton and Sussex University Hospital NHS.
[2] Department of Paediatric Opthalmology, Sitapur Eye Hospital and Regional Institute of Opthalmology, Sitapur, Uttar Pradesh, India.

Address of Correspondence
Dr. Shilpi Sethi
Clinical Fellow Anaesthetics Brighton and Sussex University Hospital NHS.
E-mail: shilpisethi77@gmail.com

Combating Airway Issues with Elective Use of an I Gel in a Child with Goldenhar Syndrome

Abstract

Introduction: Goldenhar syndrome is an oculoauriculovertebral spectrum attributed to the developmental anomalies of the first and second brachial arches. Its typical presentation in children with hemifacial microsomia poses a dual challenge for the anaesthesiologist on account of difficult airway often compounded with systemic abnormalities.
Case report: We describe a case report wherein a 5 year female presented to the oculoplastic clinic of our hospital for surgical removal of limbal dermoid under general anaesthesia. Airway examination revealed classical facial asymmetry with underdevelopment of jaw bone coupled with protruding incisors. A predicted difficult airway, more so in a child led us to choose an anaesthesia technique with preservation of spontaneous breathing and planned use of supraglottic device in the form of an I Gel for airway management.
Conclusion: The aim of this case report is to highlight the anaesthetic implications of this not so uncommon entity presenting to ophthalmology and ENT clinics. A thorough preoperative assessment, adequate preparedness and alternative plans are keys for successful airway management in such syndromic children.
Keywords: Goldenhar syndrome, hemifacial microsomia, I Gel

References

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