Spinal anesthesia for cesarean section in a patient with Ehlers-Danlos syndrome, classical subtype: a case report

Vol 5 | Issue 2 | May-Aug 2019 | page: 10-12  | Alberto Pastore, Francesca Piccini


Authors: JAlberto Pastore [1], Francesca Piccini [2]

[1] Department of Anesthesia and Intensive Care, University of Pisa, Stabilimento di
Cisanello, via Paradisa 2, 56124, Pisa, Italy.
[2] Department of Anesthesia and Critical Care Medicine, Azienda Ospedaliera
Universitaria Pisana, Stabilimento di Santa Chiara, via Roma 67, 56126, Pisa, Italy.

Address of Correspondence

Dr. Alberto Pastore,
Department of Anesthesia and Intensive Care, University of Pisa, Stabilimento di
Cisanello, via Paradisa 2, 56124, Pisa, Italy.
E-mail address: alberto.pastore@gmail.com


Abstract

Ehlers-Danlos syndrome includes thirteen subtypes, with different characteristics and clinical implications. There are no guidelines to help clinicians managing patients affected by this syndrome, but from 2014 recommendations exist. These patients have an increased anesthetic risk, both for general and regional technique. We describe the choice of anesthesia in a 34 years old pregnant woman, affected by Ehlers-Danlos syndrome classical subtype, who underwent cesarean section. Literature shows case reports about pregnancy and delivery in different subtypes, but not in classical one. We chose to perform a spinal block, with success.

Keywords: Ehlers-Danlos syndrome, Classical subtype, Pregnancy, Cesarean section, Spinal anesthesia.


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How to Cite this Article: Pastore A, Piccini F. Spinal anesthesia for cesarean section in a patient with Ehlers- Danlos syndrome, classical subtype: a case report. Journal of Anaesthesia and Critical Care Case Reports May-Aug 2019; 5(2):10-12. 

 


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