Vol 7 | Issue 1 | January-April 2021 | Page 14-17 | Diana T. Phan, John Le
Author: Diana T. Phan , John Le 
 Department of Anesthesiology, Olive View-UCLA Medical Center, Sylmar, California, United States of America.
Address of Correspondence
Dr. Diana T. Phan,
Department of Anesthesiology, Olive View-UCLA Medical Center, Sylmar, California, United States of America.
Pediatric ANCA- Associated Vasculitis Presenting with Acute Postoperative Subglottic Stenosis: A Case Report
Introduction: Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) often present with nonspecific constitutional symptoms. However, there has been increasing recognition of a subgroup of young, female AAV patients who are at higher risk for isolated subglottic airway disease.
Case Presentation: We report a rare case of a 17-year-old female with undiagnosed ANCA-associated vasculitis who presents with acute, life threatening subglottic stenosis requiring emergent intubation after routine surgery.
Conclusion: Much of the research on ANCA-associated vasculitis have been based on adult cases, however many pediatric patients may not follow the same diagnostic and clinical presentations. Clinicians should be vigilant in recognizing a subgroup of vasculitis patients who are often young, female, and have a higher prevalence of subglottic stenosis. Symptoms should be promptly worked up and initiation of immunosuppressive therapy is necessary to prevent life threatening complications and end-organ damage.
Keywords: ANCA-associated vasculitis, Subglottic stenosis, Granulomatosis with polyangiitis.
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|How to Cite this Article: Phan DT, Le J Pediatric A | NCA- Associated Vasculitis Presenting with Acute Postoperative Subglottic Stenosis: A Case Report | Journal of Anaesthesia and Critical Care Case Reports | January-April 2021; 7(1): 14-17.